目的　提高对PNHLB的X线表现与临床病理的认识。方法　报告 5例经手术病理证实的PNHLB的X线平片和临床病理所见 ,并作文献复习。结果　X线表现主要有 3种类型 :(1)浸润型骨质破坏 ,2例 ;(2 )溶骨性骨质破坏 ,2例 ;(3 )囊样骨质破坏 ,1例。 4例为B淋巴细胞型 ,1例为T淋巴细胞型。结论　该病少见 ,其特点为临床症状与X线表现两者不相一致 ,确诊依靠病理检查。 Objective To improve the understanding of X-ray findings and clinicopathology of PNHLB. Methods Five X-ray plain film and clinical pathology findings of PNHLB confirmed by pathology were reported and reviewed in the literature. Results There were three main types of X-ray manifestations: (1) invasive bone destruction, 2 cases; (2) osteolytic bone destruction, 2 cases; (3) cystic bone destruction, 1 case. 4 cases were B lymphocyte type and 1 case was T lymphocyte type. Conclusion The disease is rare, characterized by clinical symptoms and X-ray findings are not consistent, the diagnosis depends on pathological examination.