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儿童枕叶癫痫是一种特殊的癫痫综合征,我院于1990年1月~1993年9月收治6例典型病例,报道如下.临床资料男3例,女3例,首次发作年龄:2岁、3岁、5岁各1例,6两岁3例,平均年龄4.7岁.临床症状:首发年龄为2岁、3岁的2例,表现为大发作,其余4例均有典型的发作性视觉症状(有不同程度的黑蒙,视幻觉,移动的光点),其中3例接着出现偏侧阵挛,1例出现频繁呕吐.6例均足月顺产,既往史及家族史无殊;智力正常.EEG检查:皆有枕部典型的高幅棘波或尖波、棘慢综合波,其中右枕、左枕及双枕部各2例.3例行头颅CT平扫均未见异常.治疗:用鲁米那治疗3例,其中2例近期未见发作,1例仍有每周1~2次黑蒙;用丙戊酸钠治疗1例近期未见再发;苯妥英钠治疗2例,均仍有视觉症状,但较轻,无阵挛及大发作.
Children with occipital lobe epilepsy is a special kind of epilepsy syndrome, our hospital in January 1990 to September 1993, 6 cases were treated, reported as follows.Clinical data of 3 males and 3 females, the first attack age: 2 years old , 3 years old, 5 years old in each case 1, 6 years old in 3 cases, mean age 4.7 years old. Clinical symptoms: 2 years old, 2 years old, 3 years old, showed a large attack, the other 4 cases have typical attack Visual symptoms (with varying degrees of darkness, visual hallucinations, moving light spots), of which 3 cases followed by clonic clonus, 1 case of frequent vomiting .6 cases were full term, history and family history without special; Normal intelligence.EEG examination: Jieyou typical high-amplitude spikes or sharp wave spikes, spine slow synthesis wave, including the right pillow, left pillow and double pillow in 2 cases .3 cases of skull CT were no abnormalities . Treatment: 3 cases with luminal therapy, of which 2 cases have not seen a recent attack, 1 case is still 1 to 2 times a week darkness; sodium valproate treatment of a recent case of no recurrence; phenytoin sodium treatment 2 Cases, are still visual symptoms, but lighter, no clonus and major attack.