先天性单侧脑室，临床上比较少见，我科曾于1995年3月8日出现1例，现报告如下：患者付某某．男，2岁，以发热，嗜睡2天入院，无呕吐。既往健康。家族史：父母均健康，非近亲结婚，母孕期否认有药物、毒物及放射线接触史，其兄长智力差。查体体温：385℃，神志清，应答自如，反 Congenital unilateral ventricle, clinically rare, my department had on March 8, 1995 1 case, are as follows: The patient Fu Moumou. Male, 2 years old, admitted to hospital with fever and lethargy for 2 days without vomiting. Past health. Family history: both parents are healthy, non-relatives get married, pregnant women denied the existence of drugs, poisons and radiation exposure history, the poor intelligence of his brother. Physical examination temperature: 385 ℃, clear consciousness, responsive, anti