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美国心脏病协会(AHA)提出了新的心肌病的定义和分类。新定义的心肌病不仅包括心肌的机械功能障碍,还包括心肌离子通道病等。根据器官受累情况,AHA将心肌病分为原发性和继发性两大类。前者病变局限于心肌,为数较少;后者为全身性疾病的一部分。原发性心肌病又分为遗传性、混合性(遗传和非遗传)和获得性3个亚类。混合性包括扩张型心肌病和原发性限制型心肌病;获得性者包括心肌炎、应激性心肌病(Tako-Tsubo综合征)等。
The American Heart Association (AHA) proposed the definition and classification of new cardiomyopathy. The newly defined cardiomyopathy includes not only the mechanical dysfunction of the myocardium, but also the myocardial ion channel disease and the like. According to organ involvement, AHA classifies cardiomyopathy into primary and secondary. The former is limited to myocardial lesions, the number is less; the latter part of the systemic disease. Primary cardiomyopathy is divided into genetic, mixed (genetic and non-genetic) and acquired three sub-categories. Mixed include dilated cardiomyopathy and idiopathic restrictive cardiomyopathy; acquired include myocarditis, stress cardiomyopathy (Tako-Tsubo syndrome) and so on.