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目的通过病例报道及文献复习探讨呼吸道黏膜角化病的临床特点,提高临床医师对该病的认识。方法报告收治的1例呼吸道黏膜角化病及相关文献复习。结果患者临床表现为胸痛、发热,CT示气道点状钙化灶。纤支镜示会厌白色颗粒物附着,气管、双侧支气管黏膜见大小不等颗粒状结节,支气管腔内少量灰色脓性分泌物。培养有曲霉菌和铜绿假单胞菌生长。病理示气管黏鳞状上皮化生、角化亢进,黏膜上皮下局灶钙化。诊断呼吸道黏膜角化病。给予抗感染及对症治疗症状缓解。结论呼吸道黏膜角化病是一种罕见病,无特异性临床表现及辅助检查结果,气管镜在诊治过程中发挥了重要作用。
Objective To investigate the clinical features of respiratory mucosal keratosis through case reports and literature review, and to improve clinicians’ understanding of the disease. Methods Report of 1 case of respiratory mucosal keratosis and related literature review. Results The clinical manifestations of patients with chest pain, fever, CT showed airway calcification. Bronchoscopy showed epiglottis white particles attached to the trachea, bilateral bronchial mucosa see size ranging from granular nodules, a small amount of bronchial lumen purulent discharge. Culture with Aspergillus and Pseudomonas aeruginosa growth. Pathological tracheal sticky squamous metaplasia, hyperkeratosis, submucosal focal calcification. Diagnosis of respiratory mucosal keratosis. Give anti-infection and symptomatic treatment of symptoms. Conclusion Respiratory mucosal keratosis is a rare disease, nonspecific clinical manifestations and ancillary examination results. The bronchoscope plays an important role in the diagnosis and treatment.