神经 皮肤黑色素沉着序列症 ,是外胚层黑色素细胞先天性发育异常所致的全身多处巨大黑色素痣、斑和脑脊膜黑色素细胞增生浸润产生的一种临床综合征[5] 。自 186 1年报告以来 ,查阅近十年国外文献报告尸解证实 40例 ,国内仅 4例。本病极为罕见 ,现将我院 1例报告如下。病例　患 Neurodermatic melanocytic sequelae, is a clinical syndrome caused by hyperplasia of multiple melanocytic melanomas, plaques and meningococcal melanocytes caused by congenital dysplasia of ectodermal melanocytes [5]. Since the report was made in 1861, 40 cases of the autopsy confirmed by foreign literatures in recent ten years and only 4 cases in China were reported. The disease is extremely rare, now a hospital in our report as follows. Case of illness