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报告1例单发色素性紫癜样蕈样肉芽肿。患者女,51岁。左上肢斑疹10年余。皮肤科检查:左上肢屈侧一约12 cm×10 cm近椭圆形黄红色斑,境界清楚,压之褪色不明显,其上有针头大瘀点及黄褐色斑。皮损组织病理检查:角化过度,基底细胞液化变性,可见淋巴细胞亲表皮及Pautrier微脓肿;真皮浅层淋巴细胞呈带状浸润,红细胞外逸,含铁血黄素沉积,真皮中、下层血管、神经及小汗腺等附属器周围淋巴细胞浸润;部分淋巴细胞核大、染色质深而呈不典型性。免疫组化:CD3及CD4阳性细胞弥漫并可见阳性细胞亲表皮,CD8阳性细胞散在分布,CD7、CD20、CD79α及CD56均阴性。诊断:色素性紫癜样蕈样肉芽肿。
Report 1 case of single pigmented purpura-like mycosis fungoides. Female patient, 51 years old. Left upper limb spot more than 10 years. Dermatology examination: a left upper limb flexor about 12 cm × 10 cm nearly oval yellow-red spots, the realm of clear, fading pressure is not obvious, there are needle big petechia and brown spots. Skin lesions histopathological examination: hyperkeratosis, basal cell liquefaction degeneration, progenitor cells of the lymphocytes and Pautrier micro abscess; dermal shallow lymphocytes ribbon infiltration, erythrocyte efflux, hemosiderin deposition, the dermis, the lower vessel , Nerve and sweat gland and other appendages around the lymphocyte infiltration; part of the large lymphocyte nuclei, chromatin deep and was atypical. Immunohistochemistry: CD3 and CD4 positive cells were diffuse and the progenitor cells of positive cells were seen. CD8 positive cells were scattered and CD7, CD20, CD79α and CD56 were negative. Diagnosis: Pigment purpura-like mycosis fungoides.