To the editor:A 7-month-old appeared with acyanosis,an Ⅲ/6 continuous murmur at left stal border and weak femoral pulses.Electrocardiography presented biventricular enlargement with strain.Chest X-ray showed asymmetric bilateral pulmonary blood flow.Echocardiography revealed absence of right pulmonary artery (RPA),aortic coarctation (CoA),patent ductus arteriosus (PDA),moderate to severe tricuspid regurgitation,enlargement of right atrium and right ventricle.Cardiac catheterization and angiogram were performed under general anesthesia.The main pulmonary artery was extended only by the left pulmonary artery (LPA).A small isolated RPA was shown by right pulmonary vein wedge angiography,and there were fine collateral vessels into the right lung firom right brachiocephalic artery and the descending aorta.The right ductus arteriosus closed with a diverticulum left in the base of the innominate artery in this left aortic arch.The long tube-shaped left ductus was patent with 3 mm diameter,and there was preductal discrete aortic coarctation with systemic pressure gradient 34 mmHg (Figure 1):QP/QS was 1.25 and PVR was 8.2 wood unit.