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原著标题:Ueber einen Fall von Dystrophia musculorum mit posi-tivem Rückenmarksbefunde.刊载杂志:Wien.Med.Wochenschr,1890,40:1796-1798.原著作者:Werdnig Guido(1862-?)摘译:患儿3岁,双亲健康,出生1个月时四肢活动正常,10个月左右双下肢肌力开始降低,此后逐渐出现双下肢、骨盆带、后背部的肌肉萎缩及不全麻痹。进而出现坐立及抬头困难,睡眠时眼睑不能完全闭合,并逐渐出现吞咽困难症状。查体时发现腱反射消失,保持有皮肤反射及感觉功能,括约肌功能呈正常状态。入院后3周死于呼吸障
Original title: Ueber einen Fall von Dystrophia musculorum mit posi-tivem Rückenmarksbefunde published magazine:. Wien.Med.Wochenschr, 1890,40: 1796-1798 author of the original:. Werdnig Guido (? 1862-) Excerpt: children 3 years old, Parents health, normal limb activity at 1 month of birth, muscle strength began to lower in both lower extremities after 10 months, then gradually appeared in both lower extremities, pelvic zone, back and muscle atrophy paraplegia. And then there is difficulty sitting and looking up, sleep eyelids can not be completely closed, and gradually swallowing symptoms. Check the body found tendon reflex disappeared, to maintain skin reflex and sensory function, sphincter function was normal. 3 weeks after admission died of respiratory failure