论文部分内容阅读
目的:研究心肌致密化不全患者的临床特征及预后。方法:对超声心动图诊断的心肌致密化不全36例患者,进行症状、心电图、超声心动图及随访等资料分析。结果:36例患者中9例呈家族集聚发病例,19例为散发病例,8例未进行家系筛查。17例以心力衰竭为主要表现,13例以心悸为主要表现,6例无明显症状。随访资料完整者32例,左室进行性增大17例,血栓形成及血栓事件4例,死亡1例。结论:心肌致密化不全主要表现为心力衰竭、心房颤动、缓慢性心律失常,预后较差,有较高的血栓事件。
Objective: To study the clinical features and prognosis of patients with myocardial densification. Methods: Thirty-six cases with incomplete myocardial densification diagnosed by echocardiography were analyzed with data of symptoms, ECG, echocardiography and follow-up. Results: Nine of 36 patients were familially clustered, 19 were sporadic and 8 were not screened. 17 cases of heart failure as the main performance, 13 cases of palpitations as the main performance, 6 cases without obvious symptoms. Complete follow-up data 32 cases, 17 cases of progressive ventricular enlargement, thrombosis and thrombosis in 4 cases, 1 died. Conclusion: The main manifestations of myocardial densification are heart failure, atrial fibrillation and bradyarrhythmia, with poor prognosis and high incidence of thrombosis.