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神经纤维瘤病(von Recklinghausen 氏病)是胚胎外胚层及中胚层发育异常所致的疾病。临床常以皮肤色素斑及随年龄俱增的多发性皮肤与其它组织的肿瘤为特征,最多见为表皮纤维瘤,纤维软疣及神经纤维瘤,也可同时发生脑(脊)膜瘤及胶质瘤。国内自1952至1980年共报道55例,其中伴有中枢神经系统损害的仅19例。我院自1970至1982年共收治本病患者8例,其中伴有中枢神经损害者4例,结合文献报告如下。
Neurofibromatosis (von Recklinghausen’s disease) is a disorder caused by dysplastic embryonic and mesodermal development. Clinically often pigmented skin and age with the increase of multiple skin and other tissues of the tumor is characterized by the most common epidermal fibroids, fibromyalgia and neurofibroma, but also can occur simultaneously brain (spinal) meningioma and plastic Tumor. China reported a total of 55 cases from 1952 to 1980, of which only 19 cases accompanied by central nervous system damage. Our hospital from 1970 to 1982 were treated in this patient in 8 cases, of which 4 cases accompanied by central nervous system damage, combined with the literature as follows.