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３０余年收治５例血友病Ａ患儿患有外科疾病或误诊为外科疾病。其中３例术前未诊断出血友病，术中、术后伤面及切口渗血不止，经抢救痊愈。详细询问出血史对诊断血友病有重要参考价值，最终需经凝血酶原时间（ＰＴ）、凝血酶原消耗试验（ＰＣＴ）、Ｂａｇｇ＇ｓ凝血活酶生成试验（ＴＧＴ）、白陶土部分凝血活酶时间（ＫＰＴＴ）等检查确诊。对已发生出血、渗血者输入正常人新鲜血、血浆或Ⅷ因子浓缩剂是最有效的治疗方法。提出对已确诊为血病Ａ患儿发生外科疾病的处理原则。
More than 30 years treated 5 cases of hemophilia A children with surgical diseases or misdiagnosed as surgical diseases. Among them, 3 cases had no diagnosis of hemophilia preoperatively, bleeding more than intraoperative and postoperative wounds and incisions, and recovered after rescue. For more information about the history of bleeding for the diagnosis of hemophilia has important reference value, eventually required by the prothrombin time (PT), prothrombin depletion test (PCT), Bagg’s thromboplastin production test (TGT), clay part of the clotting Live enzyme time (KPTT) and other tests confirmed. For bleeding, bleeding into the normal new blood, plasma or factor VIII concentration is the most effective treatment. Put forward the diagnosis of a disease in children with surgical treatment of A disease.