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目的探讨泌尿道肾源性腺瘤的临床病理特征、诊断与鉴别诊断。方法对2例泌尿道肾源性腺瘤的临床、组织学及免疫组织化学特点进行分析,结合相关文献讨论。结果 2例患者年龄分别为27岁和48岁,男、女各1例,病变部位分别位于膀胱和肾盂。临床缺乏特异性症状,主要表现为血尿或尿路刺激症状。组织学上肿瘤呈腺样、管状或乳头状结构,被覆立方或柱状上皮,异型性不明显;免疫组织化学(EnVision法)瘤细胞示CKpan、CK7、Pax-2、CD10、Vim均阳性,P63局灶阳性,CK5/6、PSA、P504S均阴性,Ki67呈低表达。结论肾源性腺瘤是发生在泌尿道少见的良性肿瘤,它的正确诊断需要结合病理形态及免疫组化指标,并与相关疾病鉴别。
Objective To investigate the clinicopathological characteristics, diagnosis and differential diagnosis of urothelial neoplasms. Methods The clinical, histological and immunohistochemical features of 2 cases of urinary nephrectomy were analyzed, and the related literatures were discussed. Results The age of 2 patients was 27 years old and 48 years old respectively. One case was male and one female. The lesions were located in bladder and renal pelvis respectively. Clinical lack of specific symptoms, mainly for hematuria or urinary tract irritation. Histologically, the tumors showed adenoid, tubular or papillary structures, covered with cubic or columnar epithelium, and atypia was insignificant. Immunohistochemistry (EnVision) showed positive cells of CKpan, CK7, Pax-2, CD10 and Vim, Focal positive, CK5 / 6, PSA, P504S were negative, Ki67 was low expression. Conclusion Nephrogenic adenoma is a rare benign tumor that occurs in the urinary tract. Its correct diagnosis requires the combination of pathological features and immunohistochemical markers and identification of related diseases.