单侧原发的肺动脉发育不全是很少见的先天性疾病。在三个医院小儿呼吸科研究了8例(3男,5女)患该病的儿童(随访中位时间11年,从6个月到10年)。确诊的中位数年龄为4岁。临床表现包括反复的呼吸道感 Unilateral primary pulmonary hypoplasia is a rare congenital disease. Eight children (3 males and 5 females) with the disease were studied in three hospital pediatric respiratory departments (median follow-up of 11 years, from 6 months to 10 years). The median age at diagnosis was 4 years. Clinical manifestations include repeated respiratory sensation