胚胎型横纹肌肉瘤属高度恶性的一种肿瘤,其临床特点,发病年龄及其生物学行为均不同于成人型横纹肌肉瘤。本型常见于儿童,其发病率与神经母细胞瘤、Wilms瘤相似。少数可见于成人。肿瘤可原发于全身多处,常早期浸润邻近组织,并向淋巴结及远方转移,预后恶劣。国外文献报导较多,我们曾见一例临床上以皮肤结节、发热等为主要表现,诊 Embryonic rhabdomyosarcoma is a highly malignant tumor, its clinical features, age of onset and biological behavior are different from adult rhabdomyosarcoma. This type is common in children, and its incidence is similar to that of neuroblastoma and Wilms’ tumor. A few can be found in adults. Tumors may occur at multiple sites throughout the body and often infiltrate adjacent tissues in early stages, metastasize to lymph nodes and distant sites, and have a poor prognosis. There have been many reports in foreign countries. We have seen a clinical case of skin nodules and fever as the main manifestations.