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柏—查二氏综合征(Budd-Chiari Syn-drome)又称肝静脉阻塞综合征,小儿极为少见,现报告一例。杨××,男,10岁,住院号298676,以间断反复鼻衄1年,发热、右上腹部胀痛20天于1986年5月8日入院,鼻衄经局部压迫可停止。尚伴皮肤搔痒,乏力及纳差,当地按“肝炎”治疗,症状未改善。近2年来常有脓血样大便,服消炎药可好转,但常反复发作。查体:体温38.6℃,脉搏100次/分,呼吸22次/分,体重25公斤,腹围65cm,
Parker - check two syndrome (Budd-Chiari Syn-drome), also known as hepatic veno-occlusive syndrome, very rare in children, a report is now reported. Yang × ×, male, 10 years old, hospital number 298676, intermittent repeated epistaxis for 1 year, fever, upper right abdominal pain for 20 days in May 8, 1986 admission, epistaxis by local oppression can be stopped. Still with itchy skin, fatigue and anorexia, according to the local “hepatitis” treatment, the symptoms did not improve. Nearly 2 years of pus and blood often stool, anti-inflammatory drugs can be improved, but often repeated attacks. Physical examination: body temperature 38.6 ℃, pulse 100 beats / min, breathing 22 beats / min, weight 25 kg, abdominal circumference 65cm,