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肝的间叶错构瘤是一罕见的囊性损害,可能是属于先天性的疾病,而非真正新生物,肉眼检查其病灶是由不规则的囊肿组成。显微镜检查呈现丰富胶原结缔组织,可表现为成熟的间叶或看来像原生间叶。囊肿或假囊肿的大小及所含液体各不相同。肝细胞和胆小管常呈不规则的排列。 Maresch曾于1903年第一次在一个五岁女孩身上发现间叶错构瘤,其症状已超过三年。其后又有30例报告。间叶错构瘤常表现为无痛性上腹部的肿块,且可快速增大。最常见于三岁以下的儿童。而年龄较长的病人也曾有报告。单纯基于临床表现或化验检查难以将这些良性肿瘤与恶性肿瘤相鉴别。血管造影被认为是手术前最有效的诊断方法.
Hepatic medullary hamartoma is a rare cystic lesion that may be a congenital disease, rather than a true new creature, whose gross lesions consist of irregular cysts. Microscopic examination reveals a rich collagenous connective tissue that can appear as a mature mesenchyme or appear as a primary mesenchymal leaf. The size of cysts or false cysts and the fluid they contain varies. Liver cells and bile canal often have an irregular arrangement. Maresch first discovered mesenchymal hamartoma in a five-year-old girl in 1903. Her symptoms have been more than three years. Then there were 30 reports. Metaphyseal hamartoma usually presents as a painless mass in the upper abdomen and can rapidly increase. The most common are children under the age of three. The older patients also reported. It is difficult to distinguish these benign tumors from malignant tumors based solely on clinical manifestations or laboratory tests. Angiography is considered to be the most effective method of diagnosis before surgery.