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目的总结先天性膈疝的临床特征及误诊原因,以提高对本病的认识。方法对我院收治的先天性膈疝2例患儿的临床资料进行回顾性分析。结果男1例56天,女1例4岁,主要临床特点:二例均以呼吸道感染为首发症状,1例为支气管肺炎伴难以纠正的心衰表现,另1例为反复呕吐、腹痛难以缓解的胃肠道症状,2例经摄X线胸片后确诊,并及时转外科治疗。结论先天性膈疝临床表现多种多样,缺乏特异性,并发症多,严重者危及生命;对有呼吸、消化或/和循环系统疾病症状者应常规摄胸片有助于提高诊断率,为尽早治疗提供有利时机。
Objective To summarize the clinical features and causes of misdiagnosis of congenital diaphragmatic hernia in order to improve the understanding of this disease. Methods The clinical data of 2 cases of congenital diaphragmatic hernia admitted to our hospital were analyzed retrospectively. Results There were 1 male, 56 female, 1 female, 4 years old. The main clinical features were as follows: two cases were respiratory tract infection as the first symptom, one case was bronchopneumonia with refractory heart failure, and the other case was repeated vomiting. Of gastrointestinal symptoms, 2 cases were confirmed by X-ray film, and promptly transferred to surgical treatment. Conclusion The clinical manifestations of congenital diaphragmatic hernia are diverse, lack of specificity, complications and serious life-threatening. For patients with symptoms of respiratory, digestive or / and circulatory diseases, conventional radiography should help to improve the diagnosis rate. Treatment provides a favorable opportunity.