目的 :探讨罕见的肾盂内翻性乳头状瘤的诊断治疗。方法 :结合 10例肾盂内翻性乳头状瘤复习国外文献 ,对诊断及治疗原则进行讨论。结果 :肾盂内翻性乳头状瘤多以血尿就诊 ,IVU检查肾盂充盈缺损 ,CT片示肾盂占位性病变。 3例行内窥镜检查见有蒂灰色实性团块 ,病理诊断为内翻性乳头状瘤。 7例行肾、输尿管、膀胱部分切除 ,3例内窥镜下局部切除、电灼术 ,随访三年无变化。结论 :此属良性病变可能与长期慢性炎症刺激以及对化学性致癌物质敏感不同导致 ,虽为良性 ,但易同时或异时变发泌尿系恶性肿瘤 ,治疗以内窥镜治疗首选 ,术后随访十分重要 Objective: To investigate the diagnosis and treatment of rare renal pelvis papilloma. Methods: 10 cases of inverted papilloma were retrospectively reviewed and the principles of diagnosis and treatment were discussed. Results: Renal inverted papilloma mostly hematuria treatment, IVU examination of renal pelvis filling defect, CT showed renal pelvis space occupying lesions. 3 routine endoscopic examination of the pedunculated gray solid mass, pathological diagnosis of inverted papilloma. 7 cases of kidney, ureter, partial resection of the bladder, 3 cases under local endoscopic resection, electrocautery, no change in follow-up for three years. Conclusion: This benign lesion may be caused by long-term chronic inflammatory stimulation and sensitivity to chemical carcinogens. Although benign, it is easy to cause malignant neoplasm of urinary tract at the same time or different time. The treatment is the first choice of endoscopic treatment and the follow-up of 10 important