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目的 探讨肌炎型眼眶特发性炎性假瘤的临床特点。方法 回顾分析我院 1 978年 1月~1 999年 1 2月特发性眼眶炎性假瘤病例 ,每例均有完整的临床特点、影像表现、诊断和治疗结果等记录。随访时间为 1周到 9年 (平均 4个月 )。结果 2 0 9例眼眶特发性炎性假瘤中 ,1 6例 ( 8% )属于肌炎型眼眶特发性炎性假瘤。其中男 6例 ,女 1 0例 ;右眼 6例 ,左眼 7例 ,双眼 3例 ;平均就诊年龄39岁。以眼球运动受限与斜视 ( 87 5 % )、复视 ( 6 8 8% )、眼球突出 ( 6 2 5 % )为最常见表现 ,眼部充血 ( 4 3 8% )和疼痛 ( 4 3 8% )是与其它类型斜视不同的重要特点。各条眼外肌中 ,上直肌受累最常见 ( 6 2 5 % ) ,其次为外直肌 ( 4 3 8% ) ,内直肌 ( 31 % )和下直肌 ( 31 % )。经全身激素或激素联合局部放射治疗后 ,治愈率为 5 6 % ,有效率为 75 % ,复发率为 75 %。结论 肌炎型是特发性眼眶炎性假瘤中较少见的临床亚型之一 ,以上直肌受累最常见 ,其次为外直肌、内直肌与下直肌。全身激素或激素联合放射治疗的治愈率只有 5 6 % ,而复发率高达 75 %。如何提高治愈率与减少复发率是今后努力的方向
Objective To investigate the clinical features of myophthalmitis or idiopathic inflammatory pseudotumor. Methods The clinical data of idiopathic orbital inflammatory pseudotumor from January 1978 to January 1999 in our hospital were retrospectively analyzed. Each case had complete clinical features, imaging findings, diagnosis and treatment results. Follow-up time ranged from 1 week to 9 years (mean, 4 months). Results Of 209 patients with orbital idiopathic inflammatory pseudotumor, 16 (8%) were myositis orbital idiopathic inflammatory pseudotumor. Including 6 males and 10 females; right eye in 6 cases, left eye in 7 cases, binocular in 3 cases; the average age of 39-year-old clinic. The most common manifestations were eye movement restriction and strabismus (87.5%), diplopia (68.8%) and prominent eyeball (62.5%), eye congestion (43.8%) and pain %) Is different from other types of strabismus important features. In each extraocular muscle, the upper rectus muscle involvement was the most common (65.5%), followed by the lateral rectus (48.3%), the medial rectus muscle (31%) and the lower rectus muscle (31%). The whole body hormones or hormones combined with local radiotherapy, the cure rate was 56%, the effective rate was 75%, the recurrence rate was 75%. Conclusions Myositis is one of the less common clinical subtypes of idiopathic orbital inflammatory pseudotumor. The most common is the above rectus muscle, followed by the lateral rectus, medial rectus and inferior rectus. Systemic hormones or hormones in combination with radiotherapy cure rate was only 56%, while the recurrence rate as high as 75%. How to improve the cure rate and reduce the recurrence rate is the direction of future efforts