Budd-Chiari综合征即肝静脉下腔静脉阻塞综合征,为一较少见的疾病。目前,国外对其研究已逐渐深入,约累积病例数百例。国内临床工作者对该病也有所认识,根据各地资料,已报告有46例。然遗憾的是,大多为生前误诊,尸解证实。据称,1947年以前,国外文献中97例,生前诊断者仅10例。国内资料中继发于癌肿7例,无1例系生前临床诊断。笔者近遇及1例继发于肝癌之 Budd-Chiari syndrome, a hepatic vena cava obstruction syndrome, is a rare disease. At present, foreign studies on it have gradually deepened, about hundreds of cumulative cases. Domestic clinical workers are also aware of the disease, according to local information, has been reported in 46 cases. However, unfortunately, most of them were misdiagnosed as before, confirmed by autopsy. Allegedly, before 1947, 97 foreign literature, prenatal diagnosis only 10 cases. Domestic information in the secondary to cancer in 7 cases, no case of prenatal clinical diagnosis. Nearly 1 case of the author and secondary to liver cancer