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颅缝早闭可致神经、精神和视力紊乱,而致因是诱发大脑异常发育的颅内高压。治疗方法包括索状截骨,根治性截骨和重建颅骨截除,但这些手术均着重于美容,缓解颅内压和再骨化,而忽视面中部发育的远期疗效。作者提出一种治疗Crouzon综合征和Apert综合征的功能性方法。 1980~1996年,作者共对311例各种颅缝早闭患者进行治疗。方法分三步:①出生后6个月,按Powiertoaski氏法行包括有关骨缝、前颅窝和蝶额裂的广泛截骨;②6~10岁时按Tessier氏法作标准的额部前移及Lefort Ⅲ型截骨;③术后4~6周使用DeLaire面弓作
Suture craniosynostosis can cause nerve, mental and visual disorders, and due to abnormal brain development caused by intracranial hypertension. Treatment includes cord osteotomy, radical osteotomy and reconstruction of skull amputation, but these operations are focused on beauty, relieve intracranial pressure and re-ossification, while ignoring the long-term effect of midface development. The authors propose a functional approach to treat Crouzon syndrome and Apert syndrome. From 1980 to 1996, a total of 311 patients with various craniosynostosis patients were treated. Methods are divided into three steps: ① 6 months after birth, according to Powiertoaski's line includes extensive osteotomy osteochondral, anterior fossa and butterfly fissure; ② 6 to 10 years old by Tessier's method as the standard forehead And Lefort Ⅲ osteotomy; ③ 4 to 6 weeks after the use of DeLaire bow