报告我国首例进行性多灶性白质脑病,临床上表现为精神症状后出现以锥体外系及锥体束损害为主的进行性弥漫性脑部病变,两大脑半球白质有散在众多与血管分布无关的脱髓鞘小病灶,并具有正常少突胶质细胞消失和星形胶质细胞增生肥大的病理特征,未发现核内包涵体的存在。 Reported the first case of progressive multifocal encephalopathy in our country, clinical manifestations of mental symptoms after the extrapyramidal and pyramidal tract lesions of the progressive diffuse brain lesions, white matter scattered in both cerebral hemispheres and vascular distribution Irrelevant demyelinating small lesions, with the disappearance of normal oligodendrocytes and pathological features of astrocyte hypertrophy and hypertrophy, the presence of nuclear inclusions was not found.