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目的探讨额叶癫疒间临床发作表现及视频脑电图特征。方法对2005年6月-2007年6月长程脑电监测者中符合额叶癫疒间的20例患儿临床发作及视频脑电图特征进行回顾性分析。结果20例患儿共监测到临床发作50次。临床发作形式主要表现为:偏转发作、姿势性强直、过度运动,部分患儿发作合并有发声或自动症。白天夜间均有发作,夜间发作较多。半数以上发作间期脑电图无癫疒间波。临床发作期脑电图大多数有异常,但不典型,可表现为额极及额区的尖波节律、慢节律、快节律、棘节律或尖-慢波、棘-慢波,或以上混合,有时可波及到颞区、中央区甚至泛化全导。发作频繁者背景活动有慢化。卡马西平、奥卡西平可以减少发作甚至控制发作。结论额叶癫疒间临床发作以偏转发作、姿势性强直、过度运动为主,以夜间为主,持续时间短。剥夺睡眠长程脑电监测可提高额叶癫疒间诊断率,特别是发作期脑电图,有利于额叶癫疒间的诊断与鉴别诊断。卡马西平、奥卡西平治疗有效。
Objective To explore the clinical manifestations of frontal lobe epilepsy and video EEG features. Methods The clinical seizures and video-EEG features of 20 children who met the frontal lobe epilepsy between June 2005 and June 2007 were retrospectively analyzed. Results A total of 50 cases of clinical seizures were detected in 20 children. Main forms of clinical seizures are: deflexion, posture tonic, excessive exercise, some children with seizures or vocal seizures. Both have attacks during the day and night, night attacks more. More than half of the episodes of epileptic EEG without epilepsy wave. EEG most of the clinical attack period is abnormal, but not typical, can be expressed as frontal and frontal area of the sharp wave rhythm, slow rhythm, fast rhythm, spinous rhythm or sharp-slow wave, spike-wave, or more mixed , Sometimes can be spread to the temporal area, the central area and even the generalization of all-inclusive. The frequent episodes of background activity have moderated. Carbamazepine and oxcarbazepine can reduce attacks and even control seizures. Conclusion The clinical seizures of frontal lobe epilepsy are deflecting seizure, postural rigidity and excessive exercise, mainly at night and short duration. Deprivation of sleep Long-range EEG monitoring can improve the diagnosis of frontal lobe epilepsy, especially the onset of EEG is conducive to the diagnosis and differential diagnosis of frontal lobe epilepsy. Carbamazepine, oxcarbazepine treatment effective.