原始神经外胚层肿瘤(primitiveneuroectodermaltu mors,PNETs)是指一组发生于中枢交感神经系统(中央型)和周围肌肉、骨骼组织(周围型),由原始未分化的小圆细胞构成的恶性肿瘤,它在儿童及青少年中发病率较高。自1973年Hart和Earle[1]首先提出颅内PNETs至今,关于其命名一直存在争 Primitive neuroectodermal tumors (PNETs) refers to a group of central nervous system in the central nervous system (central) and the surrounding muscle and skeletal tissues (peripheral type), from primitive undifferentiated small round cell malignant tumor, it In children and adolescents in the higher incidence. Since 1973, Hart and Earle [1] first proposed intracranial PNETs so far, there has been debate about its naming