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本病为重点侵犯主动脉及其主要分支的非特异性慢性炎症性疾患,病变累及动脉壁全层,广泛纤维增生以致管腔狭窄闭塞。常用的同义名有 Takayasu 病或综合征、无脉病、主动脉弓综合征、多发性大动脉炎等。好发于青年女性,儿童较少。Ueda 复习文献321例中14岁以下者仅占5.61%,Lande等报告23例中儿童期发病者约1/3。中国医学
The disease is mainly focused on violations of the aorta and its major branches of the non-specific chronic inflammatory disease, lesions involving the entire wall of the artery, extensive fibrovascular stenosis and occlusion. Common synonymous Takayasu disease or syndrome, no pulse disease, aortic arch syndrome, multiple arteritis and so on. Occur in young women, fewer children. Ueda reviewed literature 321 cases accounted for only 5.61% of 14-year-olds, Lande et al reported 23 cases of childhood onset about 1/3. Chinese medicine