小儿门静脉海绵样变性 (CTPV)是因门静脉主干部分或完全阻塞所导致肝门区和十二指肠韧带及其周围形成许多向肝性扩张迂曲的静脉血管瘤样侧支循环 ,进而引起肝外型门静脉高压。我们从 1994年 5月至 2 0 0 3年 11月共手术治疗CTPV16例。报告如下。本组男 13例 ,女 3例。年龄 4～ Pediatric portal vein cavernous degeneration (CTPV) is due to the main portal vein partial or complete obstruction caused by the portal area and duodenal ligaments and the formation of many around the liver to expand tortuous venous angioma-like collateral circulation, which led to extrahepatic Portal hypertension. We co-operated CTPV in 16 cases from May 1994 to November 2003. The report is as follows. The group of 13 males and 3 females. Age 4 ~