本文报告1例原发性肺淋巴肉瘤,并复习文献,对其病理及临床特点进行讨论。本瘤可能来源于支气管粘膜淋巴组织或血管外膜,在肺内形成境界不清的肿块,沿肺间质浸润,常不累及支气管和血管,远方转移少。临床上常误诊为肺慢性炎症。病灶上应与小圆形未分化癌区別。手术切除后,预后常较良好。 This article reports a case of primary pulmonary lymphosarcoma and reviews the literature to discuss its pathological and clinical features. The tumor may originate from the bronchial mucosal lymphoid tissue or the adventitia of the blood vessels, forming an unclear mass in the lung, along the interstitial infiltrate of the lung, often involving the bronchus and blood vessels, and the distant metastasis is small. Often misdiagnosed as chronic pulmonary inflammation. The lesions should be distinguished from small round undifferentiated carcinomas. After surgery, the prognosis is often better.