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目前多认为Behcet氏病(BD)是一种全身性自身免疫性疾病,其基本病变是血管及血管周围炎。本病的临床表现除反复发生口腔、阴部溃疡及眼部病变外,可侵犯全身多种脏器,如皮肤、关节、肺、消化道、心及大血管和神经系统等,其中以皮肤病变为多见,以中枢神经、消化道、心及大血管受损的预后为差。 BD神经病变早在1941年Knapp即报道一例,1944年Berlin报道一例尸解所见之后引起重视,陆续有报道。1954年Cavara等将有神经病变的BD称之为neuro-Behcet’s Syndrome。BD神经病变的发生率文献报道不一,国内报道约2.6~16.2%,这
Behcet’s disease (BD) is currently considered a systemic autoimmune disease, the basic lesion is vascular and perivascular inflammation. In addition to the clinical manifestations of the disease recurring oral, genital ulcers and ocular lesions, the body can invade a variety of organs, such as skin, joints, lungs, digestive tract, heart and blood vessels and nervous system, etc., of which the skin lesions More common to the central nervous system, digestive tract, heart and large vessel damage prognosis is poor. As early as 1941, Knapp reported a case of BD neuropathy, which was reported after a case of autopsy was seen in Berlin in 1944, one after another reported. In 1954 Cavara and other will have neuropathy BD called neuro-Behcet’s Syndrome. The incidence of BD neuropathy varies reported in the literature, the domestic coverage of about 2.6 ~ 16.2%, which