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原发性肺动脉高压病因未明,且预后差。口服血管扩张剂虽可使少数病例肺循环阻力降低、心排血量增加,但也可引起严重而顽固的体循环低血压。前列环素(epoprostenol,flolan,prostacyclin)静脉应用,半衰期短,易于调整剂量使之产生所要求的血流动力学效应,如有不良反应则停药后立即消失。方法研究对象为10(女6,男4)例重度原发性肺动脉高压患者,平均年龄30岁。其中8例右室衰竭。口服血管扩张剂无效,病情迅速恶化。静脉滴注
Etiology of primary pulmonary hypertension is unknown, and the prognosis is poor. Oral vasodilator although a small number of cases can reduce pulmonary resistance, cardiac output increased, but can also cause severe and stubborn systemic hypotension. Prostaglandin (epoprostenol, flolan, prostacyclin) intravenous use, short half-life, easy to adjust the dose to produce the required hemodynamic effects, if any adverse reactions disappear immediately after withdrawal. Methods The subjects were 10 (6 female, 4 male) patients with severe primary pulmonary hypertension, with an average age of 30 years. Eight cases of right ventricular failure. Oral vasodilator invalid, rapid deterioration. Intravenous infusion