1975年JERVELL,LANGE-NIELSEN等人报告非血缘关系的双亲生的6个孩子,其中有4人患有先天性耳聋,并在3～4岁时,有晕厥发作.对其中3人描记了心电图,均见Q-T间期延长.这6个病例中有3人分别于4、5、9岁时死亡.这样的具有先天性耳聋,同时合并特异的心电图改变的病例,其后也有30余例报告. 1963年ROMANO,1964年WARD分别报告了不伴有先天性耳聋,但有同样的心电图改变和晕厥发作而致急死的病例,以后将这样病例称为R-W综合 1975 JERVELL, LANGE-NIELSEN, who reported 6 non-blood relatives of six children, of whom 4 were congenital deafness, and in 3 to 4 years old, have a syncope attack on which 3 were traced ECG , All see the extension of QT interval.Three cases of six cases died at the age of 4, 5, and 9. Such cases of congenital deafness combined with specific ECG changes, there are more than 30 cases 1963 ROMANO, 1964 WARD were reported not accompanied by congenital deafness, but the same ECG changes and episodes of syncope caused by acute cases of death, the case later referred to as RW synthesis