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Peutz—Jeghers 综合征(下称PJS)的三大特征:口唇和口腔粘膜色素斑点,胃肠道多发性息肉及家族遗传史,已为大家所熟知。但关于本病的息肉恶变及与生殖系统肿瘤的关系仍有争论。本文根据我们所遇到的3例PJS 并结合文献对上述问题进行探讨。
The three major characteristics of Peutz-Jeghers syndrome (hereinafter referred to as PJS): lip and oral mucosa pigment spots, multiple polyps of the gastrointestinal tract and family history are well known. However, there are still controversies about the malignant transformation of polyps and the relationship with reproductive system tumors. This article discusses the above problems based on the three cases of PJS we encountered and the literature.