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亚急性坏死性淋巴结炎(SNL)临床少见,类似与病毒相关性吞噬血细胞综合征(VAHS)的SNL文献尚无报告,现报告1例。患儿,男性,11岁。因间歇性高热,白细胞及血小板减少,右颈部淋巴结肿大人院。查体,患儿虽高热,但一般情况良好,双侧颈部淋巴结可触及并有轻度压痛,右颈部淋巴结如拇指大小。其余部位淋巴结不肿大,肝脾未触及。颈部淋巴结活检发现细胞凝固性坏死,核碎裂,滤泡不清楚,正常淋巴结结构消失。坏死灶周围泡沫样组织细胞增生,
Subacute necrotizing lymphadenitis (SNL) clinical rare, similar to the virus associated with phagocytic hemorrhagic syndrome (VAHS) SNL literature has not been reported, is reported in 1 case. Children, male, 11 years old. Due to intermittent high fever, white blood cells and thrombocytopenia, right cervical lymph node enlargement hospital. Physical examination, children with high fever, but generally good, bilateral cervical lymph nodes can be touched and mild tenderness, right cervical lymph nodes such as thumb size. The remaining part of the lymph nodes is not enlarged, liver and spleen not touched. Cervical lymph node biopsy found that cell coagulation necrosis, nuclear fragmentation, follicle is not clear, the normal lymph node structure disappears. Necrosis around the foam-like tissue cells proliferation,