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1951年,Alexander等首先以血清凝血酶原转变加速素(SPCA)为题,详细叙述了一例先天性出血性疾病,即现在认为的凝血因子Ⅶ缺乏症。国内曹氏近来报道一家族4例,并述及马、徐二氏各一例,共计6例。此症通常为单一凝血因子缺乏,但也有合并数个凝血因子同时缺乏者(Chung)。 病例介绍 患者为4(1/2)岁男孩,主因鼻衄和齿龈渗血于1980年5月15日入院治疗。此后又分别于同年8月15日和12月20日先后两次入院治疗。每次均经输血后症状消失而出院。体格检查:神智清醒,发育营养一般,除鼻衄体征外,头、颈、胸、腹,以及四肢关节未见异常。神经系检查也无异常改变。
In 1951, Alexander et al. First described the case of congenital hemorrhagic disease, now known as factor VII deficiency, with the title of Serum Prothrombin Conversion Accelerator (SPCA). Domestic Cao recently reported a family of 4 cases, and to mention the horse, Xu Er’s a case, a total of 6 cases. This disorder is usually a single factor lack of coagulation factors, but also combined with the absence of several coagulation factors (Chung). Case description The patients were 4 (1/2) year old boys who were admitted to hospital on May 15, 1980 due to epistaxis and gum bleeding. Since then, respectively, in August 15 the same year and December 20 has twice admitted to hospital. Each time the symptoms disappeared after transfusion and discharged. Physical examination: sober, developmental nutrition in general, except for nasal discharge signs, head, neck, chest, abdomen, and limbs and joints were normal. No abnormal changes in neurological examination.