目的:探讨肝脏局灶性结节样增生(FNH)的临床特点、病理特征、影像学表现及鉴别诊断,以期对其进行准确诊断和合理治疗。方法:笔者回顾性总结近期收治的1例,结合患者临床资料进行文献综述。结果:随访8个月,患者恢复良好,复查肿瘤标志物、腹部CT未见异常。结论:FNH是一种少见的良性肿瘤性疾病,多数无特异性临床表现,CT和MRI增强扫描能提高对FNH的诊断率。对有症状者或与恶性病变难以鉴别者应积极行手术治疗。 Objective: To investigate the clinical features, pathological features, imaging findings and differential diagnosis of focal nodular hyperplasia (FNH) in the liver in order to accurately diagnose and treat it. Methods: The author retrospectively reviewed 1 case recently admitted, combined with the clinical data of patients for literature review. Results: After 8 months of follow-up, the patients recovered well and the tumor markers were reviewed. Abdominal CT was normal. Conclusion: FNH is a rare benign neoplastic disease, most of which have no specific clinical manifestations. CT and MRI enhanced scan can improve the diagnostic rate of FNH. Surgical treatment of symptomatic or difficult to identify with malignant lesions should be actively performed.