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本病极为罕见,Skalka1979年统计国外文献不超过24例。我国纪秀香1948年报告一例,30年后严密又报告两例。我院近年遇到两例,报告如下: 例1 黄××女 39岁 20余年前开始夜间视力差。三年前眼前有黑影,近来增多,经治疗无效。1982年3月25日初诊;家族中无类似眼病,父母非血族联姻。体检未见异常。视力:右眼0.4,近视力:0.5;左眼:0.4,近视力:0.4。双外眼及眼前节正常。眼压正常。眼底:右眼玻璃体有尘状及絮状混浊,视盘色稍发黄,边缘清楚,其周围有环形色素脱失区。视网膜动、静脉均较细,于静
The disease is extremely rare, Skalka 1979 nationality design over more than 24 cases. Jiuxiuxiang 1948 report of a case of China, 30 years later, closely reported two cases. In recent years, our hospital encountered two cases, the report is as follows: Example 1 yellow × × female 39 years old 20 years ago began to have poor eyesight at night. There are dark shadows three years ago, recently increased, the treatment is invalid. March 25, 1982 newly diagnosed; no similar eye disease in the family, parents non-kin marriage. No abnormal physical examination. Eyesight: right eye 0.4, near vision: 0.5; left eye: 0.4, near vision: 0.4. Double outer eyes and anterior segment normal. IOP normal. Fundus: right eye vitreous and flocculent clouds of dust, disc color slightly yellow, clear edges, around the annular pigment loss zone. Retina, veins are thin, in the static