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病例报告:患儿为11岁男孩,患慢性中性粒细胞减少和复发性中耳炎。免疫学检查发现其血清免疫球蛋白降低,同种凝集素缺乏,植物血凝集素(PHA)引起的淋巴细胞转化正常,但对共同抗原组的延迟过敏反应缺如。平均白细胞计数低于100/mm~3。患儿出现水痘的典型水疱,在发病4天内,相继出现成批的水疱超过正常典型的儿童期水痘。第5天胸部X线检查发现间质性肺炎,即开始静脉注射青霉素。以后2日内,体温升至40℃,呼吸加快,50次/分。全身布满小水疱与痂皮,两肺可闻弥漫性罗音,淋巴细胞与粒细胞的绝对计数分别为500/mm~3与600/mm~3。
Case Report: A 11-year-old boy with chronic neutropenia and recurrent otitis media. Immunological examination found that serum immunoglobulin decreased, the same lectin deficiency, Phytohemagglutinin (PHA) caused by normal lymphocyte transformation, but the common antigen group delayed the lack of allergic reactions. Average white blood cell count below 100 / mm ~ 3. Children with chickenpox typical blisters, within 4 days of onset, have emerged in batches of blisters more than normal typical childhood chickenpox. Day 5 chest X-ray examination found interstitial pneumonia, that is, intravenous penicillin. After 2 days, body temperature rose to 40 ℃, breathing speed up, 50 beats / min. Whole body covered with small blisters and crusts, two lungs can be heard diffuse rales, absolute count of lymphocytes and granulocytes were 500 / mm ~ 3 and 600 / mm ~ 3.