横纹肌肉瘤是恶性程度很高的软组织肿瘤之一,眼眶及泌尿道多见,发生在鼻、鼻窦及鼻咽部者少见,杂志报道仅两例。本6例鼻、鼻窦及鼻咽部横纹肌肉瘤,均经病理证实,长期观察,1例生存近10年。本组6例除1人50岁外,3例7岁以下,2例22岁,平均19岁。男性发病率较高。其临床表现以鼻阻为常见症状,次为鼻出血、头痛、耳痛、流涕、耳溢液,偶 Rhabdomyosarcoma is one of the most highly malignant soft tissue tumors, common in the orbit and the urinary tract, and rare in the nasal, paranasal and nasopharynx. Only two cases are reported in the journal. The 6 cases of nasal, sinus and nasopharyngeal rhabdomyosarcoma, were pathologically confirmed, long-term observation, 1 case of survival nearly 10 years. The group of 6 patients except one 50 years old, 3 cases under 7 years old, 2 cases 22 years old, average 19 years old. Male incidence is higher. The clinical manifestations of nasal resistance as a common symptom, followed by epistaxis, headache, earache, runny nose, ear discharge, even