患者钱×女30岁农民住院号168679患者父母近亲结婚,四肢细长,指、趾尤为显著。双眼晶体脱位、白内障、眼球震颤,诊断为Marfan 氏综合征。入院前20天,手掌击伤左眼,视物不清。入院时,视力右眼0.1,左眼0.01,矫正不应。双晶体向下方半脱位(左眼较右眼约低1.5mm),不均匀混浊,左眼明显。左眼底可见灰白色隆起。B 超提示视网膜脱离。右眼底5点位近赤道部有一小圆裂孔,无视网膜脱离。90年9月7日行左眼晶体摘除术。术中玻璃体脱出,术后瞳孔上移。视网膜呈漏斗型脱离,下方明显,12—8点位锯齿缘有环形裂孔,裂孔宽1—1.5PD。裂孔向后延伸,距黄斑1.5PD。晶体摘除术后27天,行赤道部巩膜板层自体皮瓣环扎和巩膜缩短术,环扎带宽10mm,电凝,放出视网膜下积液1.2ml。术后眼底出现堤坝状环形隆起裂孔封闭,眼 Patient’s money × female 30 years old farmer’s hospitalization number 168679 Married parents of relatives of the patients, limbs slender, finger, toe is particularly significant. Binocular lens dislocation, cataracts, nystagmus, diagnosis of Marfan’s syndrome. 20 days before admission, the left hand eye injury, depending on the material is not clear. Admission, visual acuity 0.1, left eye 0.01, correction should not. Double crystal subluxation down to the left (about 1.5mm lower than the right eye), uneven turbidity, left eye significantly. Left eye can see gray uplift. B-Tip retinal detachment. Right eye fundus 5 points near the equator has a small round hole, no retinal detachment. September 7, 1990 left eye crystal excision. Intraoperative vitreous prolapse, postoperative pupil shift. Funnel-shaped retinal detachment, the bottom of the obvious, 12-8 point serrated edge ring hole, hole width 1-1.5PD. Holes extend backward, from the macular 1.5PD. 27 days after extraction of the lens, autologous flap cerclage and scleral buckling of the scleral plate in the equatorial region were performed. The bandage was ligated 10 mm in width and electrocoagulated to release 1.2 ml of subretinal fluid. Occurrence of embankment after the ring-shaped annular bumps closed hole, eyes