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目的:探讨儿童烟雾病的临床及影像学特征改变。方法:对20例烟雾病患儿的临床资料进行回顾性分析。结果:临床表现主要有偏瘫、头痛、癫痫发作等。磁共振(MRI)多为缺血性改变,磁共振血管成像(MRA)和数字减影动脉造影(DSA)均可显示动脉的狭窄和闭塞。结论:儿童烟雾病临床症状不典型,MRA成为本病诊断及观察病变进展的首选方法,但DSA仍为显示脑血管病变的金标准,若进行手术治疗,则需进一步作DSA检查。
Objective: To explore the clinical and imaging features of moyamoya disease in children. Methods: The clinical data of 20 patients with moyamoya disease were retrospectively analyzed. Results: The main clinical manifestations are hemiplegia, headache, seizures and so on. Magnetic resonance imaging (MRI) mostly ischemic changes, magnetic resonance angiography (MRA) and digital subtraction arteriography (DSA) can show arterial stenosis and occlusion. Conclusion: The clinical manifestations of moyamoya disease in children are not typical. MRA is the first choice to diagnose and observe the pathological changes of this disease. However, DSA is still the gold standard for displaying cerebrovascular diseases. If surgery is needed, DSA should be further performed.