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The diagnosis of pulmonary hypertension (PH) should be made by combining clinical manifestations and echocardio-graphic probability.[1] Following the confirmation of PH, the classification should begin with the more common groups[group 2 (PH due to left heart disease) and group 3 (PH due to lung diseases and/or hypoxia)],then group 4 (chronic thromboembolic PH and other pulmonary artery obstruc?tions) and finally group 1 (pulmonary arterial hypertension)and group 5 (PH with unclear and/or multifactorial mecha?nisms).[1] In this case,we demonstrate a rare scenario of obstruction-caused group 4 PH.