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1964年O′Brien证实有恶性纤维黄色瘤(MFX;即恶性纤维组织细胞瘤,MFH)存在,其发生率占纤维组织细胞瘤的1%。1978年Weiss等报道200例MFH,认为MFH是成人最常见的软组织肉瘤,以往许多病例曾被误诊为横纹肌肉瘤、脂肪肉瘤、纤维肉瘤等,必须引起重视。一、组织起源 MFH的组织起源尚有争论,存在三种学说: 1.起源于纤维母细胞,某些纤维母细胞可“转化”成组织细胞,构成双向分化,但此学说尚缺乏确切的证据。 2.O′Brien等提出MFH起源于组织细胞,它除具有吞噬作用外,部分细胞尚可转化为“功能性”纤维母细胞。它能产生网织纤维及胶元纤维。
In 1964, O’Brien confirmed the presence of malignant fibrosarcoma (MFX; malignant fibrous histiocytoma, MFH), accounting for 1% of fibrous histiocytoma. In 1978 Weiss reported that 200 cases of MFH, MFH that MFH is the most common adult soft tissue sarcoma, in the past many cases have been misdiagnosed as rhabdomyosarcoma, liposarcoma, fibrosarcoma, etc., must pay attention. First, the origin of the organization of the origin of MFH There are still controversies, there are three doctrines: 1. Originated in fibroblasts, some fibroblasts can be “transformed” into tissue cells, constitute a two-way differentiation, but this theory is still lack of exact evidence . 2. O’Brien et al. proposed that MFH originated from histiocytes. In addition to phagocytosis, some cells can be transformed into “functional” fibroblasts. It can produce reticulated fiber and plastic fiber.