论文部分内容阅读
目的探讨心肌淀粉样变性患者的临床表现,诊断及治疗;方法对我院心内科诊断的1例心肌淀粉样变性患者的临床表现,心电图和超声心动图等进行临床分析;结果心肌淀粉样变性表现为难治性充血性心力衰竭,心律失常、多浆膜腔积液、肢体低电压,在超声心动图上表现为左室室壁厚度增加,室壁活动弥慢性减弱,或有颗粒状心肌强回声等改变。结论心肌淀粉样变累及多个脏器系统,心脏超声和心电图均有特征性改变,病程进展快,预后极差。
Objective To investigate the clinical manifestations, diagnosis and treatment of patients with myocardial amyloidosis.Methods The clinical manifestations, electrocardiogram (ECG) and echocardiography of 1 patient with amyloidosis diagnosed by cardiology were analyzed retrospectively. Results Myocardial amyloidosis For refractory congestive heart failure, arrhythmia, pleural effusion, limb low voltage, echocardiography showed increased left ventricular wall thickness, ventricular wall thickening, or myocardial granular echogenic echo Change. Conclusions Myocardial amyloidosis and multiple organ systems, cardiac ultrasound and ECG have characteristic changes, the course of the disease progresses rapidly and the prognosis is very poor.