先天性母系遗传性独指,伴不发育,裂足畸形是临床上极为少见的先天性手足畸形症。国内仅见裂掌、裂足的少数病例报告,家族中也多表现为散发型,很少能见到一组的报告。本文收集整理的一家族三代九人有5例患者,足部的畸形完全类同于文献报告的“龙虾足”,手部的畸形表现为独指,伴一侧指骨完全性不发育,与文献描述 Congenital maternally inherited single, with no development, split foot deformity is clinically rare congenital hand-foot deformity. Domestic only crack palm, crack foot minority cases report, the family also showed mostly sporadic, rarely see a group report. This article collected three families and nine generations of a family of five patients, foot deformities exactly the same as reported in the literature “lobster feet” hand abnormalities showed single finger, with one side of the phalanx complete development, and the literature description