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对4例MCTD的神经系统合并症和肌症状,肌病理特点进行了初步探讨。认为MCTD的神经系统合并症从中枢神经至末梢神经呈现出多样的临床表现。MCTD的肌症状以四肢远端为著。肌活检发现轻度的肌纤维坏死和肌束膜、肌内膜的单核细胞漫润。其中2例出现了小角化纤维和群集萎缩。以上病理变化可能与合并末梢神经损伤有关。
Four cases of MCTD neurological complications and muscle symptoms, myopathic features of a preliminary study. That MCTD’s neurological complications from the central nervous to peripheral nerve showed a variety of clinical manifestations. Muscle symptoms of MCTD are distal to extremities. Muscle biopsy found mild muscle fiber necrosis and myofibroblasts, mononuclear cells infiltration of endometrial. In 2 of these cases, there were small-angle fibers and cluster atrophy. The above pathological changes may be related to the combined peripheral nerve injury.