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烟雾病为1961年铃木先生首次描述定义Moyamoya(日语烟雾的意思),是指脑底颈内动脉分叉处明显狭窄或闭塞,致使脑底部异常血管网的形成,形同袅袅的烟雾,也可密集成堆状或不规则网状,是儿童和青壮年急性脑血管病原因之一,本文就20例烟雾病的临床与影像分析总结如下。1 临床表现 20例患者,男8例,女12例,年龄3~54岁,平均(29.26±15.25)岁,<20岁6例。脑实质出血3例,2例为50岁女性,皆为左顶叶出血,1男44岁为基底节出血。原发侧脑室内出血3例,年龄3、21、28岁,1例并放射冠梗塞。1例女45岁为蛛网膜下腔出血,脑血管造影示左大脑中动脉起始部闭塞,左前交通动脉起始部动脉瘤。皆为颅脑CT证实。13例脑梗塞,年龄4~54
Moyamoya disease was first described by Mr. Suzuki in 1961. Definition Moyamoya (meaning Japanese smoke) refers to the obvious stenosis or occlusion at the bifurcation of the internal carotid artery, resulting in the formation of an abnormal network of blood vessels at the bottom of the brain, curl-like smoke, or Densely packed heap or irregular mesh, is one of the causes of acute cerebrovascular disease in children and young adults, this article on 20 cases of moyamoya disease clinical and imaging analysis is summarized as follows. A clinical manifestations of 20 patients, 8 males and 12 females, aged 3 to 54 years, mean (29.26 ± 15.25) years, <20 years old in 6 cases. Brain parenchymal hemorrhage in 3 cases, 2 cases of 50-year-old female, all left parietal lobe hemorrhage, 1 male 44-year-old basal ganglia hemorrhage. Primary intracerebral hemorrhage in 3 cases, aged 3,21,28 years, 1 case and coronary crown infarction. One case of female 45 years old was subarachnoid hemorrhage, cerebral angiography showed the occlusion of the left middle cerebral artery and the left anterior communicating artery aneurysm. All brain CT confirmed. 13 cases of cerebral infarction, age 4 ~ 54