遗传性肾炎属伴显性遗传的慢性肾脏疾患,常伴有耳疾(耳聋、中耳炎等)和视力缺陷(近视、白内障、视网膜炎或眼球震颤),故又称耳——眼——肾综合征。本病少见,易误诊为“特发性血尿”或“慢性肾炎”等。最近我们收治一例慢性肾炎,经家系调查,属遗传性肾炎。现报告如下。 Inherited nephritis is accompanied by dominant inherited chronic kidney disease, often accompanied by ear diseases (deafness, otitis media, etc.) and visual acuity defects (myopia, cataracts, retinitis or nystagmus), it is also called ear - eye - kidney syndrome Levy The rare disease, easily misdiagnosed as “idiopathic hematuria” or “chronic nephritis” and so on. Recently, we treated a case of chronic nephritis, the pedigree investigation, is a hereditary nephritis. The report is as follows.