黑色素斑-胃肠道多发性息肉综合征,又称Peutz-Jegher′s综合征(简称P-J综合征)是一种常染色体显性遗传病。现将我们收治的1例报道如下。患儿女,9岁,因反复发作性腹痛伴呕吐4年于1987年5月28日入院。4年来患儿经常出现阵发性腹痛,每次均伴有呕吐,呕吐物为胃内容物,腹痛和呕吐多在1小时左右自行缓解。病初经常出现脱肛并排出少量鲜血,在脱出的肠段肠壁上可见有杏核大红色乳头状物。近1年来患儿逐渐出现面色苍白、消瘦无力。家族中祖母及父亲唇周、口腔粘膜、手、足等处有大小不等数量较多的黑色素斑,但无明显胃肠道症 Melanoma - gastrointestinal polyp syndrome, also known as Peutz-Jegher’s syndrome (P-J syndrome) is an autosomal dominant genetic disease. We now treat one case reported as follows. Children with children, 9 years old, recurrent abdominal pain with vomiting for 4 years on May 28, 1987 admitted. 4 years, children often have paroxysmal abdominal pain, each accompanied by vomiting, vomit for the stomach contents, abdominal pain and vomiting more than 1 hour to ease themselves. The beginning of the disease often appear prolapse and excretion of small amounts of blood in the bowel wall prolapse of the apricot nuclear red papillae. In the past 1 years, children gradually appear pale, thin and weak. Family of grandmothers and fathers lip circumference, oral mucosa, hand, foot and other places ranging from the larger number of melanoma, but no obvious gastrointestinal symptoms