上皮样肉瘤是一种软组织肿瘤,常见于成年男性的皮下或筋膜下,多发于四肢而尤以上肢为最常见。临床及组织学上常可与慢性肉芽肿性炎症、滑膜肉瘤、纤维肉瘤及鳞状细胞癌等混淆而被误诊。此瘤生长缓慢,但易复发,甚至约1/3的病例可发生转移,其恶性倾向常被估计不足。大体上,肿瘤为多结节性,灰白色至灰褐色而带有棕色斑点,镜检则见其结节组成于大的、曙红深染的上皮样细胞而合併以梭形细胞,丰富的胶元及散在的淋巴 Epithelioid sarcoma is a soft-tissue tumor commonly seen in subcutaneous or subfascial areas of adult males, with multiple limbs and especially upper limbs being the most common. Clinical and histologically, it is often misdiagnosed as being confused with chronic granulomatous inflammation, synovial sarcoma, fibrosarcoma, and squamous cell carcinoma. The growth of this tumor is slow, but it is easy to relapse, and even about 1/3 of cases can metastasize, and its malignant tendency is often underestimated. In general, the tumors were multinodular, gray to gray-brown with brown spots. Microscopic examination revealed that the nodules consisted of large, blush-darkened epithelioid cells that merged with spindle cells, rich in gelatin. Yuan and scattered lymph