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目的了解原发性干燥综合征继发血小板减少性紫癜临床特征及误诊情况。方法对12例原发性干燥综合征继发血小板减少性紫癜病人的临床表现、实验室检查、误诊情况及治疗进行回顾性分析。结果12例原发性干燥综合征继发血小板减少性紫癜被误诊为特发性血小板减少性紫癜,误诊时间5个月~8年,两者临床表现、实验室检查特别是骨髓象有相似之处,明确诊断后调整为以免疫抑制剂甲氨蝶呤、环磷酰胺为主的治疗方案,血小板计数有不同程度的升高。结论原发性干燥综合征继发血小板减少性紫癜和特发性血小板减少性紫癜临床特征有相似之处,诊断特发性血小板减少性紫癜要排除继发原因特别是风湿性疾病,避免误诊。
Objective To understand the clinical features and misdiagnosis of primary thrombocytopenic purpura with Sjogren’s syndrome. Methods The clinical manifestations, laboratory tests, misdiagnosis and treatment of 12 patients with idiopathic Sjögren’s syndrome secondary to thrombocytopenic purpura were analyzed retrospectively. Results 12 cases of primary Sjogren’s syndrome secondary to thrombocytopenic purpura were misdiagnosed as idiopathic thrombocytopenic purpura, misdiagnosis time of 5 months to 8 years, both clinical manifestations, laboratory tests, especially the bone marrow has a similar Department, a clear diagnosis of adjusted to immunosuppressive agents methotrexate, cyclophosphamide-based treatment programs, platelet counts were increased to varying degrees. Conclusions There are similarities in the clinical features of idiopathic thrombocytopenic purpura and idiopathic thrombocytopenic purpura between idiopathic Sjögren’s syndrome and idiopathic thrombocytopenic purpura. The diagnosis of idiopathic thrombocytopenic purpura should exclude secondary causes, especially rheumatic diseases, and avoid misdiagnosis.